Genetic defects of autophagy linked to disease

Milana Fraiberg, Zvulun Elazar

Research output: Chapter in Book/Report/Conference proceedingChapter

Abstract

Autophagy is a highly conserved lysosomal degradation pathway responsible for rapid elimination of unwanted cytoplasmic materials in response to stressful conditions. This cytoprotective function is essential for maintenance of cellular homeostasis and is mediated by conserved autophagy-related genes (ATG) and autophagic receptors. Impairment of autophagy frequently results in a wide variety of human pathologies. Recent studies have revealed direct links between diverse diseases and genetic defects of core autophagy genes, autophagy-associated genes, and genes encoding autophagic receptors. Here we provide a general description of autophagy-related genes and their mutations or polymorphisms that play a causative role in specific human disorders or may be risk factors for them.

Original languageEnglish
Title of host publicationAutophagy in health and disease
EditorsAB Martinez, L Galluzzi
PublisherAcademic Press Inc.
Chapter13
Pages293-323
Number of pages31
ISBN (Print)978-0-12-822021-4
DOIs
StatePublished - 2020

Publication series

NameProgress in Molecular Biology and Translational Science
Volume172
ISSN (Print)1877-1173

Fingerprint

Dive into the research topics of 'Genetic defects of autophagy linked to disease'. Together they form a unique fingerprint.

Cite this